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Ectodermal dysplasias - a review of the conditions described after 1984 with an overall analysis of all the conditions belonging to this nosologic group

Newton Freire-Maia; Marta Pinheiro

Departamento de Genética, Universidade Federal do Paraná, Caixa Postal 19071, 81504 Curitiba, PR, Brasil. Send correspondence to M.P.

ABSTRACT

A total of 23 ectodermal dysplasias described after 1984 (included) or coming to our knowledge after this year was classified according to Freire-Maia's criterion (Hum. Hered. 21: 309-312, 1971) and added to all the other conditions analyzed by Freire-Maia and Pinheiro (Ectodermal Dysplasias. A Clinical and Genetic Study, Alan R. Liss, New York, 1984). An overall analysis of all of these conditions is presented.

Keywords: ectodermal; dysplasias; nosologic group.

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